About Alfa Glucosidaze-Myozyme
Class: | Enzyme replacement therapy (ERT)
Use: | Treatment of Pompe disease (glycogen storage disease type II)
Adult dose: | 20 mg/kg body weight administered every two weeks via intravenous infusion
Pediatric dose: | 20 mg/kg body weight administered every two weeks via intravenous infusion (dosing may vary based on age and weight)
Side effects: | Infusion-related reactions (fever, chills, headache), respiratory distress, nausea, vomiting, diarrhea, abdominal pain, muscle pain, and rash
Drug Class
Enzyme replacement therapy (ERT)
Uses & Indications
Treatment of Pompe disease (glycogen storage disease type II)
Storage Requirements
Store in the refrigerator at 2°C to 8°C (36°F to 46°F); do not freeze; protect from light
Manufacturer & Packaging
Manufacturer: Genzyme Europe B.V., NETHERLANDS
Package Size
1 Vial
Price & Supplier
Price in UAE: AED 2956.00
Dosage Information
Adult Dose
20 mg/kg body weight administered every two weeks via intravenous infusion
Pediatric Dose
20 mg/kg body weight administered every two weeks via intravenous infusion (dosing may vary based on age and weight)
Side Effects
Infusion-related reactions (fever, chills, headache), respiratory distress, nausea, vomiting, diarrhea, abdominal pain, muscle pain, and rash
Contraindications & Precautions
Hypersensitivity to alglucosidase alfa or any component of the formulation; caution in patients with a history of severe allergic reactions
Important Warnings
Risk of anaphylaxis; monitor for infusion reactions; patients with cardiac disease may require monitoring; consider premedication with antihistamines or corticosteroids for patients with a history of infusion reactions
Medical Disclaimer
This information is for educational purposes only and should not replace professional medical advice.
Always consult with a licensed healthcare provider or pharmacist in the UAE before taking any medication.
The information presented here is specific to medicines available in UAE pharmacies and is regularly updated
to ensure accuracy for patients and healthcare professionals in the United Arab Emirates.